Abstract
Retroperitoneal paragangliomas are rare tumors.They usually present abdominal pain and mass clinically. A literature review suggests that only a few cases have been reported so far. A case of giant retroperitoneal paraganglioma 20x30 cm in size with extraadrenal origin in a 66-year-old patient is reported alongside with its clinical presentation, diagnosis, surgical management and literature review.
Keywords: Extraadrenal paraganglioma, retroperitoneal tumor
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