Abstract

Choledochal cysts (cc), a rarely reported disease has been increasingly reported with the help of new diagnostic modalities. It consists 1% of all biliary pathologies. Majority of the reported casesare of Asian origin. Abnormal pancreatico-biliary junction, abnormal development of bile ducts and abnormal innervation of bile ducts are suggested theories in the etiology of choledochal cysts. Main symptoms are abdominal pain, jaundice and abdominal mass, which consists the classical triad of choledochal cysts. Ultrasonography and ERCP have the advantage of depicting the ductal anatomy and recognition of the abnormal pancreatico-biliary junction. The incidence of associated hepatobiliary malignancy is between 2.5-28%. For the majority of cysis, excision and Roux-Y biliary reconstruction are the recommended treatment modalities.